دوره 25، شماره 6 - ( دو ماهنامه طب جنوب 1401 )
جلد 25 شماره 6 صفحات 557-547 |
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Kalantarhormozi M R, Abbaszadeh M, Abbasi F, Vafaee E, Ghanbari Z. Introducing a Case of MEN-1 Syndrome with Classic Manifestations in Bushehr. Iran South Med J 2023; 25 (6) :547-557
URL: http://ismj.bpums.ac.ir/article-1-1703-fa.html
URL: http://ismj.bpums.ac.ir/article-1-1703-fa.html
کلانترهرمزی محمدرضا، عباس‌زاده مولود، عباسی فاطمه، وفایی الهه، قنبری زهرا. معرفی یک مورد سندروم MEN-1 با تظاهرات کلاسیک در بوشهر. مجله طب جنوب. 1401; 25 (6) :547-557
محمدرضا کلانترهرمزی1 
، مولود عباس‌زاده1 ، فاطمه عباسی1 ، الهه وفایی1 ، زهرا قنبری*2
، مولود عباس‌زاده1 ، فاطمه عباسی1 ، الهه وفایی1 ، زهرا قنبری*2
1- گروه داخلی، دانشکده پزشکی، دانشگاه علوم پزشکی بوشهر، بوشهر، ایران
2- گروه داخلی، دانشکده پزشکی، دانشگاه علوم پزشکی بوشهر، بوشهر، ایران ،z.ghanbari1986@yahoo.com
2- گروه داخلی، دانشکده پزشکی، دانشگاه علوم پزشکی بوشهر، بوشهر، ایران ،
چکیده: (2719 مشاهده)
نئوپلازی غدد درون‌ریز نوع ۱ (MEN-1) که به نام سندروم ورمر نیز شناخته می‌شود یک اختلال اتوزومال غالب است که با وقوع ترکیبی دو یا چند تومور (به طور کلاسیک غدد پاراتیروئید، پانکراس و هیپوفیز) مشخص می‌شود. به دلیل نادر بودن سندروم MEN-1 و پیچیدگی بیماری، مدیریت بالینی دشوار است و توصیه به همکاری تیم حرفه‌ای شامل: متخصص ژنتیک بالینی، غدد، گوارش، آنکولوژی، جراح غدد، جراح مغز و اعصاب، رادیولوژیست و هیستوپاتولوژیست می‌شود. در اینجا یک مورد بیمار جوان مبتلا به سندروم MEN-1 معرفی می‌شود که به علت هیپرکلسمی در بیمارستان شهدای خلیج‌فارس بوشهر بستری شد. بیمار در کودکی سابقه لیپوما داشته و در حال حاضر دچار درگیری تومورال هر سه غده کلاسیک این سندروم می‌باشد.
نوع مطالعه: گزارش موردی |
موضوع مقاله:
دستگاه غدد
دریافت: 1401/6/25 | پذیرش: 1402/2/31 | انتشار: 1402/4/13
دریافت: 1401/6/25 | پذیرش: 1402/2/31 | انتشار: 1402/4/13
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