Volume 25, Issue 6 (Iranian South Medical Journal 2023)                   Iran South Med J 2023, 25(6): 547-557 | Back to browse issues page

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Kalantarhormozi M R, Abbaszadeh M, Abbasi F, Vafaee E, Ghanbari Z. Introducing a Case of MEN-1 Syndrome with Classic Manifestations in Bushehr. Iran South Med J 2023; 25 (6) :547-557
URL: http://ismj.bpums.ac.ir/article-1-1703-en.html
Introducing a Case of MEN-1 Syndrome with Classic Manifestations in Bushehr
Mohammad REza Kalantarhormozi1 , Moulod Abbaszadeh1 , Fatemeh Abbasi1 , Elahe Vafaee1 , Zahra Ghanbari * 2
1- Department of Internal Medicine, School of Medicine, Bushehr University of Medical Sciences, Bushehr, Iran
2- Department of Internal Medicine, School of Medicine, Bushehr University of Medical Sciences, Bushehr, Iran , z.ghanbari1986@yahoo.com
Abstract:   (2004 Views)
Endocrine neoplasia type 1 (MEN-1), also known as Wermer syndrome, is an autosomal dominant disorder characterized by the combined occurrence of two or more tumors (classically parathyroid, pancreatic, and pituitary). Due to the rarity of MEN-1 syndrome and the complexity of the disease, clinical management is difficult, and it is recom-mended to collaborate with a professional team including: clinical geneticist, endocrinologist, gastroenterologist, oncolo-gist, endocrinologist, neurosurgeon, radiologist, and histopathologist. Here, a case of a young patient with MEN-1 syndrome is introduced, who was admitted to Persian Gulf Martyrs Hospital in Bushehr due to hypercalcemia. The patient had a history of lipoma in childhood and currently has tumoral involvement of all three classic glands of this syndrome.
Keywords: MEN-1, tumor, gland, parathyroid
Full-Text [PDF 494 kb]   (517 Downloads)    
Type of Study: Case Report | Subject: Endocrine System
Received: 2022/09/16 | Accepted: 2023/05/21 | Published: 2023/07/4
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